遗传性球形红细胞增多症

遗传性球形红细胞增多症6例家系调查报告

Report of 6 cases of hereditary spherocytosis observed in a family

腹腔镜脾切除术治疗遗传性球形红细胞增多症（附18例报道）

Laparoscopic Resection of Splenomegaly for Hereditary Spherocytosis ( Report of 18 Cases )

目的分析儿童遗传性球形红细胞增多症的临床特点。

Objective To analyze the clinical feature of children hereditary spherocytosis ( HS ) .

方法：7例遗传性球形红细胞增多症患者及2例家系成员的静脉血置于扫描电镜下观察。

Method : The blood samples of7 cases of HS and2 cases of their family members was observed under scanning electron microscope .

目的探讨腹腔镜巨脾切除术在小儿遗传性球形红细胞增多症治疗中的可行性及效果评价。

Objective To explore the feasibility and the efficacy of laparoscopic splenectomy of massive splenomegaly in the treatment of hereditary spherocytosis in children .

术后血液学参数改善的程度依次为遗传性球形红细胞增多症、原发性血小板减少性紫癜、自身免疫溶血性贫血。

In benign group , postoperative hematologic parameters improved in cases of hereditary spherocytosis , idiopathic thrombocytopenic purpura and autoimmune hemolytic anaemia in proper order .