法洛四联症

法洛四联症297例外科治疗

A summary on surgical treatment of 297 patients with Fallot 's tetrad

病种包括法洛四联症63例，右心室双出口5例，肺静脉畸形引流4例，其他病变10例。

Cardiac defects included 63 Fallot 's Tetralogy , 5 double-outlet of right ventricle , 4 anomalous pulmonary venous and 10 other defects .

法洛四联症的MRI诊断研究

Study of MRI on tetralogy of Fallot

不同年龄法洛四联症病人心肌血管紧张素II和心钠素含量变化的临床意义

Clinical significance of changes in angiotensin II and atrial natriuretic peptide in patients with Tetralogy of Fallot at different ages

方法30名法洛四联症病人分成两个组，A组病人肺动脉功能发育良好，B组病人肺动脉发育不良。

Methods 30 TOF patients were divided into group A ( pulmonary valves function well ) and group B ( pulmonary valves exhibit a poor function ) .

小儿法洛四联症根治术后ICU滞留危险因素分析56例法洛四联症根治术的体外循环管理

Risk factors for prolonged stay in intensive care unit in children with tetralogy of Fallot undergoing corrective surgery

方法回顾性总结法洛四联症根治术患儿32例，ASAⅢ-Ⅳ级，采用静吸复合全麻和低温体外循环。

Methods To sum up 32 infants with , ASA ⅲ - ⅳ, underwent combined intravenous inhalation anesthesia and hypothermia by-pass .

目的探讨儿童法洛四联症（TOF）的体外循环（CPB）管理方法。

Objective To retrospect the management of cardiopulmonary bypass ( CPB ) on children with tetralogy of Fallot ( TOF ) .

方法39例患者，在经食管超声心动图（TEE）的监测下，经右心房和肺动脉径路行法洛四联症矫治术。

Methods Under the guide of transesophageal echocardiography ( TEE ), 39 cases underwent transatrial and pulmonary repair of tetralogy of Fallot .

目的总结法洛四联症（TOF）合并异常冠状动脉完全矫治手术的经验。

Objective To summarize the experience of surgical treatment of tetralogy of Fallot ( TOF ) with anomalous coronary artery .

目的：总结成人法洛四联症（TOF）根治术外科治疗经验。

Objective : To summarize the experience of total correction for adult patients with tetralogy of fallot ( TOF ) .

目的探讨法洛四联症（TOF）患儿心肌细胞钙运转与心功能的关系。

Objective To explore the relationship between myocardial calcium transport and cardiac function of tetralogy of Fallot ( TOF ) children .

目的探讨磷酸肌酸钠（CP）停搏液对法洛四联症（TOF）患儿术后心功能恢复的影响及其临床应用价值。

OBJECTIVE To investigate the effect of creatine phosphate sodium on myocardium protecting in children with tetralogy of fallot after radical operation and its clinical value .

目的研究与法洛四联症（TOF）一期根治手术早期死亡相关的危险因素。

Objective To identify risk factors associated with early postoperative death in patients undergoing primary repair of tetralogy of Fallot ( TOF ) .

目的探讨法洛四联症（TOF）合并不同类型的主肺侧支动脉（MAPCA）行手术矫治的适应证、方法及效果。

Objective To evaluate the indication and operative program of complete repair of tetralogy of Fallot with major aortopulmonary collateral arteries ( TOF-MAPCA ) .

法洛四联症（TOF）合并完全性房室隔缺损1例，完全性体静脉异位连接合并TOF1例。

Patient with TOF associated with complete atrio-ventricular septal defect ; 1 patient with complete vana cava drainage to left atrium associated with TOF .

目的探讨法洛四联症（TOF）缺氧发作与右心室血浆儿茶酚胺浓度改变的关系。

Objective To study the regulation of plasma catecholamine of the right ventricle in the tetralogy of Fallot ( TOF ) patients with hypoxic spells .

目的分析法洛四联症（TOF）根治术后急性肺损伤（ALI）的原因，总结治疗体会。

Objective To analyse the reasons of acute lung injury ( ALI ) after the surgical correction of tetralogy of Fallot ( TOF ) and summarize the postoperative treatment skill .

目的比较人同种心包补片和Gore-tex补片在法洛四联症（TetralogyofFallot，TOF）分期手术中扩大右心室流出道（rightventricularoutflowtract，RVOT）的效果。

Objective To compare the difference of effect while using homograft pericardium patch and Gore-tex patch in staged repair of tetralogy of Fallot ( TOF ) to enlarge the right ventricular outflow tract ( RVOT ) .

小结：1.法洛四联症患儿心肌组织中HIRA基因的异常低表达，提示其可能参与了法洛四联症的发病机制。

The abnormal low expression of HIRA gene in myocardium of the TOF group may participate in the pathogenesis of TOF . 2 .

目的运用经食管超声心动图（TEE）对儿童法洛四联症（TOF）的右室流出道（RVOT）情况进行围术期评价。

Objective To evaluate the condition of right ventricular outflow tract ( RVOT ) during perioperative period by transesophageal echocardiography ( TEE ) in children with tetralogy of Fallot ( TOF ) .

目的对法洛四联症患者的肺动脉（PA）、左肺动脉（LPA）和右肺动脉（RPA）分支进行量化分析，探讨其临床意义。

Objective To investigate the clinical significance of quantitative analysis of pulmonary artery ( PA ), left pulmonary artery ( LPA ), right pulmonary artery ( RPA ) in total correction of tetralogy of Fallot .

方法以手术结果为标准，对59例法洛四联症患儿运用RT-3DE进行剖析诊断，并与二维超声（2DE）诊断结果比较。

Methods Fifty-nine children with TOF were diagnosed on RT-3 DE using topologic method . The results were compared with two-dimensional echocardiography ( 2 DE ) and surgical operations ( golden standard ) .

法洛四联症患儿围术期血清P-ICP、P-Ⅲ-NP、IGF-1与心肌组织胶原、基质金属蛋白酶及其抑制剂的变化及意义

Changes and Its Significance of Serum P-ICP , P - ⅲ - NP , IGF-1 and Collagens , Matrix Metalloproteinases and Their Inhibitors in Myocardial Tissue of Children with Tetralogy of Fallot During Perioperative Period

方法应用非线性动力学方法和传统的频域方法分析两组先天性心脏病&室间隔缺损（VSD）和法洛四联症（TOF）患儿术前术后心率变异的变化。

Methods By using the nonlinear dynamics method and the power spectrum method , the authors analyzed the HRV signals pre and post operation in 2 groups of CHD patients , ventricular septal defect ( VSD ) and tetralogy of Fallot ( TOF ) .

结论改良Blalock-Taussig分流术是肺动脉或左心室发育不良的重症法洛四联症患儿的有效姑息治疗方法。

Conclusion Modified Blalock-Taussig shunts were effective palliative operation in the treatment of severe tetralogy of Fallot with maldevelopment of pulmonary arteries or left ventricle .

138例法洛四联症根治术的体外循环管理

Extracorporeal circulation management on 138 cases of total correction of TOF

对法洛四联症中右心室流出道梗阻的再认识

Reevaluation of right ventricular outlet tract obstruction in tetralogy of Fallot

法洛四联症右心室流出道心肌的超微结构及力学特性

Myocardium characters of right ventricular outflow tract in Tetralogy of Fallot

法洛四联症患儿右室适应性衰竭

Failure of right ventricular adaptation in children with tetralogy of Fallot