小脑扁桃体下疝畸形

目的对小脑扁桃体下疝畸形（Chiari畸形）及合并脊髓空洞症的临床诊断与手术治疗方法探讨并分析疗效。

Objective To discuss the diagnosis and surgical treatment of Chiari malformation and syringomyelia .

目的探讨小脑扁桃体下疝畸形的发病机制及应用后颅窝减压治疗的效果。

Objective To explore the nosogenesis of Arnold chiari malformation and the therapeutic effect of the iateria of Posterior fossa decompression .

Chiari畸形是以小脑扁桃体下疝畸形为特征的先天性疾患，目前较为公认的理论是起源于胚胎中胚叶轴旁的枕骨原节发育不良所致，其诊断主要依赖于MRI。

Chiari malformation is a congenital malformation characterized with hindbrain hernia . It is generally accepted that it caused by underdevelopment of the occipital somite originating from the paraxial mesoderm . The diagnosis of Chiari malformation is mainly based on MRI .

颅后窝重建治疗小脑扁桃体下疝畸形

Posterior fossa reconstruction for the treatment of Chiari ⅰ malformation

颅底陷入症合并小脑扁桃体下疝畸形的联合手术治疗（附4例报告）

Combined operation to treat the basilar invagination complicated with chiari malformation ( a report of 4 cases )

方法对14例先天性小脑扁桃体下疝畸形合并脊髓空洞症患者，根据不同的病情采用相应的手术方式进行治疗。

Methods 14 patients with congenital tonsillar hernia deformity associated with syringomyelia had been treated with correspondent surgery depending on their case condition .

本病病因尚不完全明了，与颅颈接合部畸形如小脑扁桃体下疝畸形、产伤、脊髓损伤、炎症等多种因素有关。

Though causes of this disease are not clear , it relates to many factors such as Arnold-chiari malformation , birth trauma , spinal cord injury and the like .

方法回顾我科1995~2004年治疗的31例小脑扁桃体下疝畸形病例，对于应用后颅窝减压手术方法的27例患者进行回顾分析。

Methods Review the Arnold chiari malformation patients who accept therapy in my department from 1995 to 2004 , appreciation the therapeutic effect of patients who accept the therapeutics of Posterior fossa decompression .

结论应用后颅窝减压法治疗小脑扁桃体下疝畸形疗效明显，是治疗本病的首选。

Conclusion Posterior fossa decompression is effective in treating Arnold chiari malformation , and it is considered that the method of Posterior fossa decompression can be used as the first choice of surgical treatment .

小脑扁桃体下疝并脊髓空洞症的诊治进展小脑扁桃体下疝畸形及脊髓空洞症的手术治疗分析

Advances in diagnosis and treatment of Chiari malformation associated with syringomyelia