primary immunodeficiency

Primary Immunodeficiency Disease & A Report of 11 Cases

原发性免疫缺陷症11例

Rare Patterns of Primary Immunodeficiency Diseases in Children , Report of 3 Cases

儿童原发性免疫缺陷病的少见类型&附三例报告

Three clinically rare cases of primary immunodeficiency were reported .

本文报告了3例临床较少见的原发性免疫缺陷病。

Clinical investigation of 135 primary immunodeficiency disorders in children

儿童原发性免疫缺陷病135例临床分析

Morphological changes of primary immunodeficiency with review of literature

原发性免疫缺陷病尸检1例形态学观察及文献复习

Overview of clinical occurrence of primary immunodeficiency disorders in children

原发性免疫缺陷病临床发病情况回顾

Objective To realize the clinical features of primary immunodeficiency ( PID ) in children for early detection and diagnosis .

目的了解儿童原发性免疫缺陷病（PID）的临床特点，以助于早期识别和诊断。

When people are born with a faulty immune system , they are said to have a Primary Immunodeficiency .

出生时免疫系统不健全就是罹患了主要免疫系统不全症。

The absence of MHC II normal expression results in severe primary immunodeficiency diseases , such as the bare lymphocyte syndrome ( BLS ) .

MHcII类分子不正常表达会引起严重的免疫缺陷疾病，如裸淋巴细胞综合征（BLS）等。

Conclusions Not all children with CHD have congenital thymus aplasia or immunodeficiency . It is not certain that primary immunodeficiency is the reason why children with CHD may be prone to infection .

结论并非所有CHD患儿均伴有胸腺发育不全或免疫功能缺陷，CHD患儿易感染不一定是先天性免疫功能低下的表现。